(Subacute Spongiform Encephalopathy; CJD)
- Sporadic CJD—also called classical CJD; most common type; usually affects people aged 50 years and older
- Familial CJD—an inherited form of the disease
- Iatrogenic CJD—contracted through medical procedures, such as injections of growth hormone or receipt of corneal transplants or dura mater implants from affected donors
New variant CJD (vCJD)
—caused by eating contaminated beef products, which may cause bovine spongiform encephalopathy (BSE)
- BSE is commonly known as mad cow disease. vCJD differs from other forms of CJD because it affects younger people and has a longer average time course.
- Age: 50-75 years
- Use of cadaveric growth hormone
- Cornea transplants
- Dura mater grafts
- Family members with CJD—Approximately 10%-15% of cases are inherited
- Eating beef products produced by countries with an epidemic of BSE
- Healthcare workers who work with brain tissues
- Blood transfusion from someone with CJD
- Memory lapses
- Difficulty concentrating
- Impaired judgment
- Difficulty with speech
- Loss of coordination
- Blurred vision
- Behavior and mood changes
- Muscle spasms
- Loss of mental and physical function
- You may need to have your brain activity recorded. This can be done with electroencephalogram (EEG) .
- Images may need to be taken of your brain. This can be done with:
- You may need to have your brain's use of glucose checked. This can be done with a brain positron emission tomography (PET) scan .
- Your bodily fluids may need to be tested. This can be done with: removal of a sample of brain tissue for testing
|MRI Scan of the Brain|
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- Opiates to treat pain
- Anticonvulsive drugs to help decrease neuromuscular problems
Creutzfeldt-Jakob Disease Foundation, Inc. http://www.cjdfoundation.org
National Institute of Neurological Disorders and Stroke http://www.ninds.nih.gov
World Health Organization http://www.who.int/en
Health Canada http://www.hc-sc.gc.ca
Public Health Agency of Canada http://www.phac-aspc.gc.ca
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- Reviewer: Rimas Lukas, MD
- Review Date: 03/2013 -
- Update Date: 00/31/2013 -